Journal of Conservative Dentistry

CASE REPORT
Year
: 2014  |  Volume : 17  |  Issue : 2  |  Page : 188--191

Endodontic management of a patient with Bernard-Soulier syndrome


Dexton Antony Johns1, Reji P Gopalan1, Ganesh Tukaram Kamble2, S Vidyanath3 
1 Department of Endodontics, Government Dental College, Calicut, Kerala, India
2 Department of Prosthodontics, Government Dental College, Calicut, Kerala, India
3 Department of Oral and Maxillofacial Pathology, KMCT Dental College, Calicut, Kerala, India

Correspondence Address:
Dexton Antony Johns
Department of Endodontics, Government Dental College, Calicut, Kerala
India

Bernard-Soulier syndrome is a rare inherited disorder with giant platelets, thrombocytopenia and a prolonged bleeding time. These abnormalities are caused by genetic defects of the glycoprotein Ib/IX/V complex that constitutes the von Willebrand factor receptor on the platelet surface. We are documenting a 30-year-old female patient reported with a chief complaint of swelling in relation to right maxillary canine for 5 days. The primary treatment remains platelet transfusion. Root canal treatment was performed following platelet rich plasma transfusion. As the tooth was necrotic and had a periapical pathology post-operative bleeding was absent. The root canal treatment was uneventful and the patient was asymptomatic. Optimum oral hygiene practices were emphasized to avoid dental diseases.


How to cite this article:
Johns DA, Gopalan RP, Kamble GT, Vidyanath S. Endodontic management of a patient with Bernard-Soulier syndrome.J Conserv Dent 2014;17:188-191


How to cite this URL:
Johns DA, Gopalan RP, Kamble GT, Vidyanath S. Endodontic management of a patient with Bernard-Soulier syndrome. J Conserv Dent [serial online] 2014 [cited 2021 Oct 27 ];17:188-191
Available from: https://www.jcd.org.in/article.asp?issn=0972-0707;year=2014;volume=17;issue=2;spage=188;epage=191;aulast=Johns;type=0